A 17-month- old boy presented with 3 week history of left head tilt and a 3 day history of cessation of crawling. Developmental history- Delay in sitting independently (8 months) and crawling (12 months). Birth history and PMH were unremarkable. Neurologic examination was positive. Muscle bulk, tone, sensation, reflexes, and coordination were all within normal limits. MRI study- An expansile, enhancing, intramedullary mass from C2-T3 with an associated syrinx above and below the lesion.
He subsequently underwent complete C3 to T3 laminectomy for spinal cord decompression and tumor resection. Microscopic examination - Small fragments of neuroglial tissue with increased cellularity in a heterogeneous distribution. Images demonstrate moderately cellular proliferation of monomorphic, process-forming cells in a basophilic proteinaceous background with angiocentric nuclei. No mitosis. What…
