The congenital abnormalities associated with bilateral congenital corneal dystrophy they are as follows: Congenital glaucoma Keratoconus Anterior staphyloma Congenital absence of dust membrane Deafness is known as Cogan's syndrome Congenital hereditary endothelial dystrophy Keratoconjunctivitis sicca Medullated optic nerve fibres Conjunctival xerosis Congenital ptosis eyelids