Pseudoxanthoma Elasticum (PXE) is subretinal neovascularisations an inherited disease characterized by changes in the elastic tissue of skin eyes hear and GIT cutaneous and eye manifestations of PXE is referred as Gronblad Strandberg syndrome. The condition mainly manifests as premature atherosclerosis.
Ocular manifestations of PXE are an Angioid Streaks Optic disc drusen Atrophy of retinal pigment epithelium and outer retina d subretinal neovascularization Secondary scarring and fibrosis Macular involvement Share your views.