Phakom CNS and other parts of brain in ophthalmology, it invovcatosis is a group of conditions where there is tumor formation in CNS and other parts of brain ophthalmology in involves optic nerve and other parts of retina phacomatosis is also termed as neuro-occulo cutaneous syndrome or neurocutaneous syndrome it is embryonic ectodermal disorder. So these multisystem disorders involve the ectodermal structures like CNS the group of phakomatosis are as follows: Ataxia telengectasia   Incontinentia pigmenti Neurofibromatosis Nevoid basal cell carcinoma  syndrome Stuge webers syndrome  Tuberous sclerosis Von hippel lindau syndrome  Tumors and cysts of retina  AV ayrusym of brain and spinal cord Share your views.