A 12-year-old boy reported bilateral, progressively enlarging eyelids for five years. The orbital masses resulted in proptosis and severe cosmetic blemish. On examination, the masses were found to be firm and rubbery, extending from deep in orbit to the upper and the lower lids in both eyes. The mass appeared to be molded around the orbital structures with the expansion of the bony orbits. The patient had a history of penetrating orbital injury two years before the disease onset and had suffered vision loss in the right eye.
CT of the orbits revealed preseptal and intraorbital multi-lobulated masses in both orbits (Cover image). No significant nodal involvement was noted. Immunohistochemistry was strongly positive for skeletal muscle actin with ratchet-like forms. Source: Nigerian Journal of Clinical Practice *This case is from the Editorial Team of Docplexus and is meant for…