Goldenhars Syndrome (GHS) is a congenital syndrome complex characterised by congenital limbal dermoid with the associated presence of a preauricular skin tag or appendage. One may also notice the presence of a squint or congenital coloboma of squint or anophthalmos. But it is very rare limbal dermoid. Commonest site inferotemporal is 70 percent prevalence 1 in 10 000 or 1 in 3 500 to 5 600. The male-female ratio is 3 is to 2.
Limbal dermoids are graded as grade i 2 and 3 according to corneal involvement. Most of the patients of GHS have normal vision and intelligence only 5 to 15 percent have additional congenital anomalies. reassurance to parents is important. However, if limbal dermoid involves pupillary area and threatens vision treatment is surgical which is both visual and cosmetic lamellar keratoplasty stem cell graft amniotic membrane graft We have GHS support group of 217…
