Abstract: Hemiconvulsion-hemiplegia-epilepsy syndrome is an uncommon consequence of prolonged focal febrile convulsive seizures in infancy and early childhood. We report two cases of hemiconvulsion-hemiplegia-epilepsy syndrome who presented acutely and had striking neuroimaging findings suggestive of diffuse cytotoxic edema confined to one hemisphere as docu-mented by magnetic resonance imaging, including extensive diffusion weighted imaging abnormalities in both the cases. Keywords: HHE syndrome, developmental delay, focal febrile status epilepticus Introduction: Hemiconvulsion-hemiplegia-epilepsy (HHE) syn- drome involves sudden and prolonged unilateral sei- zures, followed by transient or permanent hemiplegia and partial epilepsy during infancy or early child- hood [1].
Extensive atrophy of the involved hemi- sphere is documented by neuroimaging. HHE syn- drome is an uncommon…
