Immunodeficiency disorders often result from long usage of drugs or serious disorders like cancers but can be occasionally inherited. The primary immunodeficiency disease (PIDs) is rare and it includes a group of 130 distinct disorders caused due to a genetic defect of the immune system. The prevalence of PIDs is 1 in 1200 of births which often includes IgA deficiency. This case is a presentation of the immunodeficiency disorder accompanied by Hodgkin’s Lymphoma (HL).
Case scenario A five-months-infant was referred to the Department of Pediatric Hematology and Oncology of the Medical Center as he had fever and skin lesion accompanied by hepatosplenomegaly (HSM) and thrombocytopenia. His parents were non-cognate, and his sister was healthy. Physical examination Hepatomegaly and splenomegaly were observed, additionally, with lymphadenopathy Laboratory Findings His initial laboratory…
