Congenital corneal dystrophy is a rare entity characterised by the presence of some unknown substance in the corneal stroma. The etiopathogenesis of this disorder is not known however here do familial genesis is a great risk factor.

Classification of corneal dystrophy contains the lesions in the cornea of an unknown aetiology which may manifest at birth. At first, the second decade of life may remain stationary or progressive then gets strong here do familial tendency of bilateral central symmetrical corneal opacity with the absence of deep vascularisation and impaired corneal sensations in corneal dystrophy unless proved otherwise.