Case presentation A 4-year-old girl was admitted to the hospital after suffering from fever for the past week. She had altered sensorium along with generalized abdominal pain and distention. Medical history The patient had a history of multiple episodes of jaundice since birth.

Laboratory examinations Total bilirubin levels:  17.4 mg/dl Direct bilirubin:  10.2 mg/dl Indirect bilirubin:  7.2 mg/dl WBC count:  15,900 /mm3 Blood ammonia levels:  129 mcg/dl  Elevated serum galactose levels Radiological examination Reformatted coronal computed tomography with dynamic contrast-enhanced angiography of the abdomen in the portal venous phase (Cover image) was performed. ##Source## Applied Radiology ## ##Disclaimer## The content provided on Docplexus is intended for educational purposes only. While we strive to ensure its accuracy, we make no warranties, explicit or implied, about the…