Cystic fibrosis is a genetic, life-threatening disease which affects the digestive and respiratory systems and that affects more than 70,000 people worldwide. CF occurs in about 1 in 3500 live births and currently, there is no cure. CF results from mutations affecting a gene that encodes for a chloride channel called the cystic fibrosis transmembrane conductance regulator (CFTR), which is essential for the regulation of salt and water movements across cell membranes.
A need for standards of medical care: The CF community wishes to ensure all patients have equal access to the highest level of multidisciplinary specialist care that is adequately resourced and encompasses the latest evidence-based therapies. So, this guideline featured to improve the quality of life and extend the life expectancy of patients with cystic fibrosis. It is hoped that these standards will also act as an aid for…
