Non-compaction cardiomyopathy (NCC), also called as spongiform cardiomyopathy, is a rare congenital cardiomyopathy that affects both children and adults. It results from the failure of myocardial development during embryogenesis. Noncompaction cardiomyopathy was first identified as an isolated condition in 1984 by Engberding and Benber. They reported on a 33 year old female presenting with exertional dyspnea and palpitations.
Investigations concluded persistence of myocardial sinusoids (now termed noncompaction). Common symptoms associated with a reduced pumping performance of the heart includes: Breathlessness Fatigue Swelling of the ankles Limited physical capacity and exercise intolerance Due to its recent establishment as a diagnosis, and it being unclassified as a cardiomyopathy according to the WHO, it is not fully understood how common the condition is. Some reports suggest that…
