Rhabdomyomas are firm, white, well-circumscribed, lobulated nodules which may have either cardiac or extracardiac location. The cardiac rhabdomyoma is the most common type of benign cardiac tumor found in infants and children, however, the extracardiac rhabdomyoma is typically of three different types which include, adult, fetal and genital type. This article is focusing on the clinical features of cardiac rhabdomyoma tumors. In the continuation of the previous article on cardiac tumors here in this article, we will be discussing on the clinical features of the Rhabdomyoma.
It is a benign tumor of the cardiac myocyte and can be single or multiple. The cells of the tumor typically contain large glycogen filled vacuoles. Rhabdomyoma is most commonly associated with tuberous sclerosis. It is an autosomal dominant disorder with a high mutation rate; involves multiple organs like brain,…
